A novel once-daily drug showed a comparable efficacy and safety profile as the standard-of-care drug in patients with cystic ...

Pancreatic insufficiency and a history of meconium ileus were independently associated with an increased prevalence of liver disease, whereas age at diagnosis of cystic fibrosis, gender ...

The North Carolina knockout mouse (Cftr tm1Unc) line: Contain a Neo cassette in exon 10 of the murine Cftr gene and exhibit a severe phenotype that includes early intestinal obstructive and ...